Fetal bilateral renal agenesis is a invariably lethal condition characterized by pulmonary hypoplasia, malformation of the genitourinary tract, cardiovascular systems, vertebral bodies or imperforated anus in more than half of the affected individuals.
The criteria for the ultrasonographic diagnosis are severe oligohydramnios, nonvisualization of the bladder, empty renal fossa, and “lying down adrenal sign”
Accurate prediction of bilateral renal agenesis is critical both for prenatal counseling of the parents and in clinical management, because bilateral renal agenesis is a uniformly fatal condition, a mother can elect termination at any time during her pregnancy.
We present a case of severe oligohydramnios diagnosed at 21 weeks and bilateral renal agenesis diagnosed at 23 weeks gestation by using ultrasonography after amnioinfusion.